Plummervinson syndrome is a rare disease characterized by difficulty swallowing, irondeficiency anemia, glossitis, cheilosis and esophageal webs. Most of the patients are white middleaged women, in the fourth to seventh decade of life, but the isderopenica has also been described in children and adolescents. Sep 01, 2006 plummervinson syndrome can be treated effectively with iron supplementation and mechanical dilation. This means that patersonkelly syndrome, or a subtype of patersonkelly syndrome, affects less than 200,000 people in the us population. Born in inverness, donald ross paterson 18631939 was an otolaryngologist. Adam brown kelly 18651941 graduated from glasgow but worked as an ent surgeon in london, berlin and vienna. Feb 14, 2019 the association of postcricoid dysphagia, upper esophageal webs, and iron deficiency anemia is known as plummervinson syndrome pvs in the united states and paterson brown kelly syndrome in the united kingdom. Patersonkelly syndrome definition of patersonkelly. Kellypaterson syndrome sideropenic dysphagia prevalence.
Plummer vinson syndrome, also known as patterson kelly brown syndrome, sideropenic dysphagia, hysterical dysphagia is a premalignant condition, in which the patient has iron deficiency anemia. Medical university of vienna, department of internal medicine iv, division of gastroenterology and hepatology, waehringer guertel 1820, a1090 vienna, austria plummervinson or patersonkelly syndrome presents as a classical triad of dysphagia, irondeficiency anemia and esophageal webs. Signos, sindromes y enfermedades con nombre propio. Get a printable copy pdf file of the complete article 533k, or click on a page image below to browse page by. We only request your email address so that the person you are recommending the page to knows that you wanted them to see it, and that it is not junk mail.
The association of postcricoid dysphagia, upper esophageal webs, and iron deficiency anemia is known as plummervinson syndrome pvs in the united states and patersonbrown kelly syndrome in the united kingdom. Jacob filho w, ferreira mlm, curiati jae, glezer m, carvalho filho e t. Orphanet journal of rare diseases plummervinson syndrome gottfried novacek 0 address. En realidad, pueden dar resultados falsos negativos o positivos.
Even though the syndrome is very rare nowadays, its recognition is important because it identifies a group of patients at increased risk of squamous cell carcinoma of the pharynx and the esophagus. Plummervinson syndrome is defined by the classic triad of dysphagia, irondeficiency anemia and esophageal webs. Apr 03, 2019 kelly paterson syndrome sideropenic dysphagia prevalence. A group of symptoms that collectively indicate or characterize a disease, disorder, or other condition considered abnormal. Victor is shocked, he doesnt know what to do now and how to spend his last days in this world. The journal of laryngology, rhinology and otology, london, 1919, 24.
Source national institutes of health nih patersonkelly syndrome as a disease. In case of significant obstruction of the esophageal lumen by esophageal web and persistent dysphagia despite iron supplementation, rupture and dilation of the web are necessary. Paterson kelly syndrome synonyms, paterson kelly syndrome pronunciation, paterson kelly syndrome translation, english dictionary definition of paterson kelly syndrome. Plummervinson syndrome can be treated effectively with iron supplementation and mechanical dilation. The term sideropenic dysphagia has also been used, since the syndrome can occur with iron deficiency sideropenia, but it is not as. Treatment with iron supplementation and mechanical widening of the esophagus generally provides an excellent outcome. Plummervinson or pattersonkelly syndrome is a rare disease characterized by the triad. Another name for plummervinson syndrome or close medical condition association. Before this terrible news, he had a girlfriend, called ana. Definition plummervinson syndrome pvs is a classical triad of postcricoid dysphagia, upper esophageal webs, and iron deficiency anemia. Sep 07, 2018 home medterms medical dictionary az list paterson kelly syndrome definition medical definition of paterson kelly syndrome medical author. Identification and followup is relevant due to increased risk of squamous cell carcinomas of the esophagus and pharynx.
Medical university of vienna, department of internal medicine iv, division of gastroenterology and hepatology, waehringer guertel 1820, a1090 vienna, austria plummervinson or paterson kelly syndrome presents as a classical triad of dysphagia, irondeficiency anemia and esophageal webs. Jan 27, 2017 born in inverness, donald ross paterson 18631939 was an otolaryngologist. Patersonbrownkelly o disfagia sideropenica es definido por disfagia, anemia ferropenica y membrana esofagica alta. Thank you for your interest in spreading the word about the bmj.
981 423 1257 74 138 914 268 716 218 884 471 1462 1555 1081 1634 1588 1201 1588 508 1325 462 161 577 698 48 19 527 184 712 365 328 583